About the 401 Project

 

Equipment World BBQ’s
to help one of their own! 

 
Meet 3 year old Lincoln Tier.

 

Lincoln Tier

Lincoln on a Forklift at
Equipment World

 

 

Lincoln Tier

 Lincoln on the Couch

 

  Nick Tier

Baby Lincoln with parents
Nick & Brookes Tier

 

 

Lincoln Tier

Lincoln chillin' by the pool

 

 

Lincoln Tier

Lincoln Tier's
wonderful smile

 

 

The Rett Syndrome Research Trust

 

 

 

The 401 Project

Lincoln Tier and the 401 Project Fundraiser 


Local Equipment World employees help International Foundation reach fundraising research goal! 

Sault Ste. Marie Equipment World's BBQSudbury Equipment World's BBQThunder Bay Equipment World's BBQ

Sault Sainte Marie #1                Sudbury #2                                         Thunder Bay #3

UPDATE: July 24, 2012

On June 7th Equipment World hosted a charity BBQ fundraiser at each location to support the “The 401 Project”.  The Rett Syndrome Foundation has been raising funds to conduct research to reverse the MeCP2 duplication syndrome, which is affecting 3 year old Lincoln Tier, the son of Equipment World employee Nick Tier and his wife Brookes at the Sault Ste. Marie division.

For a few weeks Lincoln became the “talk of the North” as Equipment World promoted the BBQ events and The 401 Project.  The response from the community, especially those in Sault Ste. Marie, was incredible!  People from every community not only supported the BBQ’s but also provided individual cash donations which were included in the overall funds raised.  The result was a generous donation of $17,000 for The 401 Project.

 CLICK BELOW TO VIEW OUR SUCCESS STORY VIDEO:

 

Executive Director of the Rett Syndrome Foundation, Monica Coenraads says “On behalf of children and adults afflicted with MECP2 Duplication Syndrome and the families who love them, I congratulate the employees of Equipment World for their incredibly successful efforts to raise research funds for this debilitating disorder.  The extraordinary employees of Equipment World have rallied in support of their colleague, Nick Tier, whose 3 year old son, Lincoln, has the disorder. Colleagues have raised an amazing $17,000.  I am pleased to report that 100% of these funds will be invested in a research project currently ongoing in the laboratory of world renowned physician-scientist, Huda Zoghbi, at Baylor College of Medicine in Houston, TX.  Dr. Zoghbi will be exploring whether the devastating symptoms of the duplication syndrome are reversible.  The three year project has a total budget of $236,000.  Reversibility of symptoms would not only give families hope but will fuel the interest of the scientific community to commit their resources to this disorder. The funds raised from Equipment World have helped catapult us over the finish line in terms of raising funds to fully commit to this project. Furthermore, there are several key projects waiting in the wings which also need funding and global fundraising efforts continue.”

MeCP2 duplication syndrome is an extremely rare condition that occurs almost exclusively in males and is characterized by moderate to severe intellectual disability. Most people with this condition also have weak muscle tone in infancy, feeding difficulties, poor or absent speech, seizures that may not improve with treatment, or muscle stiffness (spasticity). Individuals with MECP2 duplication syndrome have delayed development of motor skills such as sitting and walking. Approximately one third of people with this condition cannot walk without assistance. Many individuals with MECP2 duplication syndrome have recurrent respiratory tract infections. These respiratory infections are a major cause of death in affected individuals, with almost half succumbing by age 25.

Coenraads continues “The Rett Syndrome Research Trust (RSRT) is the premier organization exclusively devoted to global research on Rett Syndrome and related MECP2 disorders. Our goal is to heal children and adults who will otherwise suffer the effects of these disorders for the rest of their lives. In an effort to immediately leverage RSRT’s deep knowledge base of MECP2 and well established global scientific networks families affected by this syndrome recently announced the MECP2 Duplication Syndrome Fund at RSRT.  The Fund supports projects devoted to the study and means of treatment of MECP2 Duplication Syndrome. 100% of every dollar contributed is invested in research – not a single penny goes to overhead.” 

The Tier family did not want any personal compensation; their goal was to raise financial support for The 401 Project directly to help find a cure for this disorder.  Thanks to the $17,000 raised by Equipment World employees, the Rett Syndrome Foundation has reached this next research goal.  When this experiment is successful it means that children, like Lincoln, will have a better quality of life and should be able to live longer, less stressful lives.  In January 2012, 200 families affected by the MeCP2 Duplication Syndrome brought together via the internet, united to launch a global campaign to save their children.  They called the initiative “The 401 Project” where $401 for each child affected, was to be raised by April 1, 2012 to help find a cure.  The group succeeded with their first goal and has done a tremendous job creating awareness, offering support to others with the disorder and raising funds to get the initial studies underway.  To reach their phase two goal they were looking for an additional $200,000 by April 2013 to complete the research so they can launch a drug initiative to help reverse the disease in those affected.  Thanks to the $17,000 raised by Equipment World employees, they reached this next research goal.  When this experiment is successful it means that children, like Lincoln, will have a better quality of life and should be able to live longer, less stressful lives. 

After learning the success of the events, Lincoln’s mom, Brookes Tier said "I just wanted to again, Thank Equipment World for hosting this wonderful event. It was amazing to see all the people who came out to support our son Lincoln and all the other 200+ boys around the world who are stricken with this cruel disorder. I cannot put into words, how amazing and humbling this has been. It is our hope that one day soon, there will be a cure!  Our dream is closer to becoming a reality.  Thank you from the bottom of our hearts.  Lincoln is definitely one lucky little man, and has captured many hearts."

For the past three years Nick’s family has struggled to help their son, Lincoln, stay healthy as he has had multiple bouts of pneumonia and other illnesses and they have had to travel numerous times to visit the Sick Children’s Hospital in Toronto for treatment.  Lincoln is unable to speak or walk, so his parents have learned to communicate with him in other ways and have special devices so he can have mobility and yet he still smiles and seems like a happy child.  It was the hope of the Tier family to spread the word about MeCP2 disease so that others do not have to suffer alone and to one day soon know that there will be a cure to help Lincoln enjoy many more birthdays!   

Dan Tier, Lincoln’s Grandpa, had a few nice words to share "To Everyone at Equipment World, you people are what exemplifies the Northern Ontario business community and what sets it apart from the rest of Ontario and perhaps Canada. The time, energy, compassion and commitment of your people which I witnessed today on behalf of a fellow employee truly re-affirmed my belief that people in the north always arise to, and surpass my expectations. You are thoughtful, compassionate, resourceful and when the time comes, you act on those qualities."

The goal for Equipment World was to join together the forces of the 3 branch locations and to pool all funds raised for a common cause.  This was not only a fun way for the staff to work together, at a distance, but a great way to help out one of their own.  Owner Lyle Knudsen says “The efforts put forth by our employees at each location are a real testament of the quality of people who work for us.  Each year we support a charity, this year we are thrilled to know that we have been able to directly impact the lives of so many families who struggle with this disorder including one very close to our hearts, Lincoln.”

For more details about Lincoln Tier, the 401 project and to see photos from the BBQ events: http://www.equipworld.com/article/about-the-401-project-1005.asp
To make a donation and to learn more about the 401 project, MeCP2 disorder / Lincoln Tier: 
http://www.401project.com/for-lincoln/
For information about the Rett Syndrome Foundation: http://www.rsrt.org/

If you weren't able to attend the BBQ Event but want still want to help? 
You can Donate Online NOW
Donate Online NOW

ABOUT EQUIPMENT WORLD:

Equipment World Inc. provides customers across Northern Ontario with turn-key solutions to their material handling and storage needs.  We offer Equipment Sales, Leasing, Rentals and Parts, Technical design, installations and inspections, Mobile Mechanical Service and Equipment Operator Safety Training.

Headquartered in Thunder Bay, Ontario, with branch offices in Sudbury and Sault Ste. Marie, Equipment World is always sourcing new products that can create effective workplace solutions for industrial, commercial and institutional applications. 

Equipment World is proud to support local charities and has a strong network of employees who volunteer in our communities for various organizations.

For more information about this article contact:
Heather Syvitski, Marketing Director
Head Office: 988 Alloy Drive, Thunder Bay  ON  P7B 6A5
Phone: 807-623-9561 or Toll Free: 1-800-465-6955
Email: equipworld%23com|hsyvitski
Website: www.equipworld.com

For more information about The 401 Project, please contact:
Monica Coenraads, Executive Director
Phone: 203-445-0041
Email: rsrt%23org|monica
Email: http://www.rsrt.org/